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Rosai-Dorfman As a Clinical Mimicker of Relapsing Polychondritis

JAAD case reports(2020)

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摘要
Rosai-Dorfman disease is an uncommon non–Langerhans cell histiocytosis. Typical Rosai-Dorfman disease presents with bilateral cervical lymphadenopathy, fever, anemia, and polyclonal hypergammaglobulinemia. Extranodal disease has been reported in 43% of cases, with the skin involved in 10% of such cases.1 We describe an unusual instance of Rosai-Dorfman disease presenting with bilateral ear nodules and airway involvement, mimicking relapsing polychondritis.
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关键词
airway,ear,emperipolesis,histiocytosis,relapsing polychondritis,Rosai-Dorfman disease
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