Persistent Fetal Vasculature with Vascularized Cataract and Lens Cyst: A Rare and Unique Presentation

Persistent fetal vasculature may present as anterior, posterior, or mixed type. Its typical features include microphthalmia, retrolental fibrovascular membrane, stretched ciliary processes, Mittendorf dot, total cataract, and Bergmeister papilla. Atypical features described in literature are axial myopia, platyphakia, lentiglobus, and a normal sized cornea. Platy-phakia (Flat-Lens) is a term commonly used for antero-posteriorly flattened crystalline lens. It is a described but extremely rare finding in Persistent Fetal Vasculature and may represent absorption of the lens with fusion of vestigial lens remnants with retrolental fibrovascular membrane.[1] The spectrum of unusual features may also include unregressed vascular vesicular cataractous lens. The visual prognosis in PFV is generally guarded owing to the developmental anomaly and associated amblyopia, strabismus, glaucoma, and retinal pathologies.