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卡纳达-克朗凯特综合征合并肾病综合征一例

Shanghai Medical Journal(2020)

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Abstract
卡纳达-克朗凯特综合征(Cronkhite-Canada syndrome,CCS)罕见,病因不明,以胃肠道多发息肉和外胚层三联征为主要特征,临床表现为慢性腹泻、腹痛、脱发、皮肤色素沉着、指(趾)甲萎缩脱落等.现报道1例CCS合并肾病综合征患者在采用糖皮质激素联合中药治疗后症状明显改善,以供临床医师参考.
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