Kasabach-Merritt syndrome caused by giant hemangiomas of the spleen in patients with Proteus syndrome.
BLOOD COAGULATION & FIBRINOLYSIS(2007)
摘要
Proteus syndrome is a rare hamartomous disorder with highly variable manifestations of disproportionate overgrowth of body parts, epidermal nevi and vascular malformations. We describe two patients who had typical clinical and imaging Proteus syndrome features. One of most characteristic findings in these two patients was that they had giant hemangiomas of the spleen that caused Kasabach-Merritt syndrome, demonstrating clinical bleeding and disseminated intravascular coagulation laboratory alterations. The present two cases are the first report of this complication in Proteus syndrome. The patients' bleeding tendency and hemostatic defects were completely corrected after they successfully underwent splenectomy. Blood Coagul Fibrinolysis 18:505-508 (C) 2007 Lippincott Williams & Wilkins.
更多查看译文
关键词
hemangioma,Kasabach -Merritt syndrome,Proteus syndrome,spleen
AI 理解论文
溯源树
样例
![](https://originalfileserver.aminer.cn/sys/aminer/pubs/mrt_preview.jpeg)
生成溯源树,研究论文发展脉络
Chat Paper
正在生成论文摘要