Pe-568-04 a distinct and potentially more severe neurocardiac phenotype among pediatric patients with catecholaminergic polymorphic ventricular tachycardia

We identified 4 patients (pts) with Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) at our institution with intellectual/neurodevelopmental delay, all with atypical symptoms including persistent arrhythmias at baseline (e.g. including sleep), cardiac arrest without evidence of adrenergic stimulation, left ventricular non-compaction (LVNC) and/or arrhythmogenic cardiomyopathy with systolic dysfunction. There is limited data regarding INDD in CPVT.