A rare case of unilateral tonsillar epidermoid cyst

Background Epidermoid cyst is a developmental lesion with 1.6–6.9% cases found in the head and neck region. Intraoral epidermoid cyst is a rare finding and intratonsillar epidermoid cyst is even rarer, with less than 0.01% incidence. Case presentation We are reporting a case of 16 year old with complain of unilateral tonsillar enlargement since 5 months. She underwent tonsillectomy under general anesthesia, and the specimen was sent for histopathological examination. It was reported as multiple intratonsillar epidermoid cysts on final histopathological examination. Conclusion We would like to report such a case due to its rarity and to recommend the need for histopathological diagnosis after every case of tonsillectomy in order to differentiate various benign and malignant lesions for their proper management.